en coup de sabre

Definitions

Of a subtype of localised scleroderma, having a linear, atrophic depression on the frontoparietal scalp.

not-comparable

Examples

“The patient is an unusual example of bilateral scleroderma en coup de sabre with distortion of both upper eyelids, and ocular complications.”

“The clinical picture was suggestive of a combination of scleroderma en coup de sabre and facial hemiatrophy (Parry-Romberg syndrome). Distinction between Parry-Romberg syndrome and linear scleroderma with facial atrophy can be quite difficult and it has been postulated that en coup de sabre type⟳ may actually be a forme fruste of progressive facial hemiatrophy.”

“Two out of 7 patients with scleroderma en coup de sabre also had morphea elsewhere. These findings strongly favor a close⟳ relationship between PFH and scleroderma.”

“Linear scleroderma en coup de sabre is a particular form⟳ of linear scleroderma that may not truly be related to the other forms.”

“The en coup de sabre variety probably represents a more superficial form⟳ of progressive facial hemiatrophy (the Parry–Romberg syndrome), a condition of slowly progressive atrophy of the soft tissue of half of the face⟳ with or without associated dermal sclerosis.”

CEFR level